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Neurofibromatosis
Admitted Cases
during 10 Years in Two Hospitals, Tehran, Iran
Professor M.H.
Soltanzadeh MD
Professor of Pediatrics, ID ,
Shahid Beheshti University of Medical Science ,
Tehran ,IRAN
Shirvani F, MD; Seidiabad H, MD
Assistant professor of pediatrics,
Shahid Beheshti
University , Tehran, IRAN
Professor of Pediatrics,Shahid
Beheshti University,Tehran, IRAN
GP,Tehran,
IRAN
Abstract
Purpose:
To recognise the signs and symptoms of neurofibromatosis and its
complications among patients admitted in Imam Hosein and Mofid
Hospitals during 1990-2000, Tehran, Iran.
Methods:
This existing data study was accomplished on hospital records of
patients admitted due to neurofibromatosis during these 10 years.
Demographic characteristics, presenting signs and symptoms, and
complications of the disease were recorded.
Results:
Sixteen patients including 8 males and 8 females were admitted due
to neurofibromatosis. Mean (SD) age was 7.6 + - 5.6 years
and the age range was 6 – 22 years , including 11 under the
age 10. The chief presenting complaints were multiple subcutaneous
nodules, vertebral deformities, carpal or cervical masses, gait
disorders, ophthalmic disorders, seizures, headache, pruritus,
speech disorders, ataxia, and gastrointestinal bleeding: and the
most common signs were cafe au lait spots, neurofibromata, and
freckles.
Conclusion:
Multiple neurofibromata, multiple skeletal disorders cafe au lait
spots are suggesting for neurofibromatosis.
Key words:
Neurofibromatosis, Existing data study, Iran. |
